Source Id |
NCBI (Entrez) Gene Id |
Gene Symbol |
Gene Description |
ABCB7 |
22 |
ABCB7 |
ATP binding cassette subfamily B member ... |
ACAA1 |
30 |
ACAA1 |
acetyl-CoA acyltransferase 1 [Source:HGN... |
ACAA2 |
10449 |
ACAA2 |
acetyl-CoA acyltransferase 2 [Source:HGN... |
ACADM |
34 |
ACADM |
acyl-CoA dehydrogenase medium chain [Sou... |
ACADSB |
36 |
ACADSB |
acyl-CoA dehydrogenase short/branched ch... |
ACADVL |
37 |
ACADVL |
acyl-CoA dehydrogenase very long chain [... |
ACAT1 |
38 |
ACAT1 |
acetyl-CoA acetyltransferase 1 [Source:H... |
ACO2 |
50 |
ACO2 |
aconitase 2 [Source:HGNC Symbol;Acc:HGNC... |
AFG3L2 |
10939 |
AFG3L2 |
AFG3 like matrix AAA peptidase subunit 2... |
AIFM1 |
9131 |
AIFM1 |
apoptosis inducing factor mitochondria a... |
ALAS1 |
211 |
ALAS1 |
5'-aminolevulinate synthase 1 [Source:HG... |
ALDH6A1 |
4329 |
ALDH6A1 |
aldehyde dehydrogenase 6 family member A... |
ATP1B1 |
481 |
ATP1B1 |
ATPase Na+/K+ transporting subunit beta ... |
ATP5A1 |
498 |
ATP5F1A |
ATP synthase F1 subunit alpha [Source:HG... |
ATP5B |
506 |
ATP5F1B |
ATP synthase F1 subunit beta [Source:HGN... |
ATP5C1 |
509 |
ATP5F1C |
ATP synthase F1 subunit gamma [Source:HG... |
ATP5D |
513 |
ATP5F1D |
ATP synthase F1 subunit delta [Source:HG... |
ATP5E |
514 |
ATP5F1E |
ATP synthase F1 subunit epsilon [Source:... |
ATP5F1 |
515 |
ATP5PB |
ATP synthase peripheral stalk-membrane s... |
ATP5G1 |
516 |
ATP5MC1 |
ATP synthase membrane subunit c locus 1 ... |
ATP5G2 |
517 |
ATP5MC2 |
ATP synthase membrane subunit c locus 2 ... |
ATP5G3 |
518 |
ATP5MC3 |
ATP synthase membrane subunit c locus 3 ... |
ATP5H |
10476 |
ATP5PD |
ATP synthase peripheral stalk subunit d ... |
ATP5I |
521 |
ATP5ME |
ATP synthase membrane subunit e [Source:... |
ATP5J |
522 |
ATP5PF |
ATP synthase peripheral stalk subunit F6... |
ATP5J2 |
9551 |
ATP5MF |
ATP synthase membrane subunit f [Source:... |
ATP5L |
10632 |
ATP5MG |
ATP synthase membrane subunit g [Source:... |
ATP5O |
539 |
ATP5PO |
ATP synthase peripheral stalk subunit OS... |
ATP6AP1 |
537 |
ATP6AP1 |
ATPase H+ transporting accessory protein... |
ATP6V0B |
533 |
ATP6V0B |
ATPase H+ transporting V0 subunit b [Sou... |
ATP6V0C |
527 |
ATP6V0C |
ATPase H+ transporting V0 subunit c [Sou... |
ATP6V0E1 |
8992 |
ATP6V0E1 |
ATPase H+ transporting V0 subunit e1 [So... |
ATP6V1C1 |
528 |
ATP6V1C1 |
ATPase H+ transporting V1 subunit C1 [So... |
ATP6V1D |
51382 |
ATP6V1D |
ATPase H+ transporting V1 subunit D [Sou... |
ATP6V1E1 |
529 |
ATP6V1E1 |
ATPase H+ transporting V1 subunit E1 [So... |
ATP6V1F |
9296 |
ATP6V1F |
ATPase H+ transporting V1 subunit F [Sou... |
ATP6V1G1 |
9550 |
ATP6V1G1 |
ATPase H+ transporting V1 subunit G1 [So... |
ATP6V1H |
51606 |
ATP6V1H |
ATPase H+ transporting V1 subunit H [Sou... |
BAX |
581 |
BAX |
BCL2 associated X, apoptosis regulator [... |
BCKDHA |
593 |
BCKDHA |
branched chain keto acid dehydrogenase E... |
BDH2 |
56898 |
BDH2 |
3-hydroxybutyrate dehydrogenase 2 [Sourc... |
BRP44L |
51660 |
MPC1 |
mitochondrial pyruvate carrier 1 [Source... |
CASP7 |
840 |
CASP7 |
caspase 7 [Source:HGNC Symbol;Acc:HGNC:1... |
COX10 |
1352 |
COX10 |
cytochrome c oxidase assembly factor hem... |
COX11 |
1353 |
COX11 |
cytochrome c oxidase copper chaperone CO... |
COX15 |
1355 |
COX15 |
cytochrome c oxidase assembly homolog CO... |
COX17 |
10063 |
COX17 |
cytochrome c oxidase copper chaperone CO... |
COX4I1 |
1327 |
COX4I1 |
cytochrome c oxidase subunit 4I1 [Source... |
COX5A |
9377 |
COX5A |
cytochrome c oxidase subunit 5A [Source:... |
COX5B |
1329 |
COX5B |
cytochrome c oxidase subunit 5B [Source:... |
COX6A1 |
1337 |
COX6A1 |
cytochrome c oxidase subunit 6A1 [Source... |
COX6B1 |
1340 |
COX6B1 |
cytochrome c oxidase subunit 6B1 [Source... |
COX6C |
1345 |
COX6C |
cytochrome c oxidase subunit 6C [Source:... |
COX7A2 |
1347 |
COX7A2 |
cytochrome c oxidase subunit 7A2 [Source... |
COX7A2L |
9167 |
COX7A2L |
cytochrome c oxidase subunit 7A2 like [S... |
COX7B |
1349 |
COX7B |
cytochrome c oxidase subunit 7B [Source:... |
COX7C |
1350 |
COX7C |
cytochrome c oxidase subunit 7C [Source:... |
COX8A |
1351 |
COX8A |
cytochrome c oxidase subunit 8A [Source:... |
CPT1A |
1374 |
CPT1A |
carnitine palmitoyltransferase 1A [Sourc... |
CS |
1431 |
CS |
citrate synthase [Source:HGNC Symbol;Acc... |
CYB5A |
1528 |
CYB5A |
cytochrome b5 type A [Source:HGNC Symbol... |
CYB5R3 |
1727 |
CYB5R3 |
cytochrome b5 reductase 3 [Source:HGNC S... |
CYC1 |
1537 |
CYC1 |
cytochrome c1 [Source:HGNC Symbol;Acc:HG... |
CYCS |
54205 |
CYCS |
cytochrome c, somatic [Source:HGNC Symbo... |
DECR1 |
1666 |
DECR1 |
2,4-dienoyl-CoA reductase 1 [Source:HGNC... |
DLAT |
1737 |
DLAT |
dihydrolipoamide S-acetyltransferase [So... |
DLD |
1738 |
DLD |
dihydrolipoamide dehydrogenase [Source:H... |
DLST |
1743 |
DLST |
dihydrolipoamide S-succinyltransferase [... |
ECH1 |
1891 |
ECH1 |
enoyl-CoA hydratase 1 [Source:HGNC Symbo... |
ECHS1 |
1892 |
ECHS1 |
enoyl-CoA hydratase, short chain 1 [Sour... |
ECI1 |
1632 |
ECI1 |
enoyl-CoA delta isomerase 1 [Source:HGNC... |
ETFA |
2108 |
ETFA |
electron transfer flavoprotein subunit a... |
ETFB |
2109 |
ETFB |
electron transfer flavoprotein subunit b... |
ETFDH |
2110 |
ETFDH |
electron transfer flavoprotein dehydroge... |
FDX1 |
2230 |
FDX1 |
ferredoxin 1 [Source:HGNC Symbol;Acc:HGN... |
FH |
2271 |
FH |
fumarate hydratase [Source:HGNC Symbol;A... |
FXN |
2395 |
FXN |
frataxin [Source:HGNC Symbol;Acc:HGNC:3951] |
GLUD1 |
2746 |
GLUD1 |
glutamate dehydrogenase 1 [Source:HGNC S... |
GOT2 |
2806 |
GOT2 |
glutamic-oxaloacetic transaminase 2 [Sou... |
GPI |
2821 |
GPI |
glucose-6-phosphate isomerase [Source:HG... |
GPX4 |
2879 |
GPX4 |
glutathione peroxidase 4 [Source:HGNC Sy... |
GRPEL1 |
80273 |
GRPEL1 |
GrpE like 1, mitochondrial [Source:HGNC ... |
HADHA |
3030 |
HADHA |
hydroxyacyl-CoA dehydrogenase trifunctio... |
HADHB |
3032 |
HADHB |
hydroxyacyl-CoA dehydrogenase trifunctio... |
HCCS |
3052 |
HCCS |
holocytochrome c synthase [Source:HGNC S... |
HSD17B10 |
3028 |
HSD17B10 |
hydroxysteroid 17-beta dehydrogenase 10 ... |
HSPA9 |
3313 |
HSPA9 |
heat shock protein family A (Hsp70) memb... |
HTRA2 |
27429 |
HTRA2 |
HtrA serine peptidase 2 [Source:HGNC Sym... |
IDH1 |
3417 |
IDH1 |
isocitrate dehydrogenase (NADP(+)) 1 [So... |
IDH2 |
3418 |
IDH2 |
isocitrate dehydrogenase (NADP(+)) 2 [So... |
IDH3A |
3419 |
IDH3A |
isocitrate dehydrogenase (NAD(+)) 3 cata... |
IDH3B |
3420 |
IDH3B |
isocitrate dehydrogenase (NAD(+)) 3 non-... |
IDH3G |
3421 |
IDH3G |
isocitrate dehydrogenase (NAD(+)) 3 non-... |
IMMT |
10989 |
IMMT |
inner membrane mitochondrial protein [So... |
ISCA1 |
81689 |
ISCA1 |
iron-sulfur cluster assembly 1 [Source:H... |
ISCU |
23479 |
ISCU |
iron-sulfur cluster assembly enzyme [Sou... |
LDHA |
3939 |
LDHA |
lactate dehydrogenase A [Source:HGNC Sym... |
LDHB |
3945 |
LDHB |
lactate dehydrogenase B [Source:HGNC Sym... |
LRPPRC |
10128 |
LRPPRC |
leucine rich pentatricopeptide repeat co... |
MAOB |
4129 |
MAOB |
monoamine oxidase B [Source:HGNC Symbol;... |
MDH1 |
4190 |
MDH1 |
malate dehydrogenase 1 [Source:HGNC Symb... |
MDH2 |
4191 |
MDH2 |
malate dehydrogenase 2 [Source:HGNC Symb... |
MFN2 |
9927 |
MFN2 |
mitofusin 2 [Source:HGNC Symbol;Acc:HGNC... |
MGST3 |
4259 |
MGST3 |
microsomal glutathione S-transferase 3 [... |
MRPL11 |
65003 |
MRPL11 |
mitochondrial ribosomal protein L11 [Sou... |
MRPL15 |
29088 |
MRPL15 |
mitochondrial ribosomal protein L15 [Sou... |
MRPL34 |
64981 |
MRPL34 |
mitochondrial ribosomal protein L34 [Sou... |
MRPL35 |
51318 |
MRPL35 |
mitochondrial ribosomal protein L35 [Sou... |
MRPS11 |
64963 |
MRPS11 |
mitochondrial ribosomal protein S11 [Sou... |
MRPS12 |
6183 |
MRPS12 |
mitochondrial ribosomal protein S12 [Sou... |
MRPS15 |
64960 |
MRPS15 |
mitochondrial ribosomal protein S15 [Sou... |
MRPS22 |
56945 |
MRPS22 |
mitochondrial ribosomal protein S22 [Sou... |
MRPS30 |
10884 |
MRPS30 |
mitochondrial ribosomal protein S30 [Sou... |
MTRF1 |
9617 |
MTRF1 |
mitochondrial translation release factor... |
MTRR |
4552 |
MTRR |
5-methyltetrahydrofolate-homocysteine me... |
MTX2 |
10651 |
MTX2 |
metaxin 2 [Source:HGNC Symbol;Acc:HGNC:7... |
NDUFA1 |
4694 |
NDUFA1 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFA2 |
4695 |
NDUFA2 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFA3 |
4696 |
NDUFA3 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFA4 |
4697 |
NDUFA4 |
NDUFA4 mitochondrial complex associated ... |
NDUFA5 |
4698 |
NDUFA5 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFA6 |
4700 |
NDUFA6 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFA7 |
4701 |
NDUFA7 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFA8 |
4702 |
NDUFA8 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFA9 |
4704 |
NDUFA9 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFAB1 |
4706 |
NDUFAB1 |
NADH:ubiquinone oxidoreductase subunit A... |
NDUFB1 |
4707 |
NDUFB1 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFB2 |
4708 |
NDUFB2 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFB3 |
4709 |
NDUFB3 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFB4 |
4710 |
NDUFB4 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFB5 |
4711 |
NDUFB5 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFB6 |
4712 |
NDUFB6 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFB7 |
4713 |
NDUFB7 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFB8 |
4714 |
NDUFB8 |
NADH:ubiquinone oxidoreductase subunit B... |
NDUFC1 |
4717 |
NDUFC1 |
NADH:ubiquinone oxidoreductase subunit C... |
NDUFC2 |
4718 |
NDUFC2 |
NADH:ubiquinone oxidoreductase subunit C... |
NDUFS1 |
4719 |
NDUFS1 |
NADH:ubiquinone oxidoreductase core subu... |
NDUFS2 |
4720 |
NDUFS2 |
NADH:ubiquinone oxidoreductase core subu... |
NDUFS3 |
4722 |
NDUFS3 |
NADH:ubiquinone oxidoreductase core subu... |
NDUFS4 |
4724 |
NDUFS4 |
NADH:ubiquinone oxidoreductase subunit S... |
NDUFS6 |
4726 |
NDUFS6 |
NADH:ubiquinone oxidoreductase subunit S... |
NDUFS7 |
374291 |
NDUFS7 |
NADH:ubiquinone oxidoreductase core subu... |
NDUFS8 |
4728 |
NDUFS8 |
NADH:ubiquinone oxidoreductase core subu... |
NDUFV1 |
4723 |
NDUFV1 |
NADH:ubiquinone oxidoreductase core subu... |
NDUFV2 |
4729 |
NDUFV2 |
NADH:ubiquinone oxidoreductase core subu... |
NNT |
23530 |
NNT |
nicotinamide nucleotide transhydrogenase... |
NQO2 |
4835 |
NQO2 |
N-ribosyldihydronicotinamide:quinone deh... |
OAT |
4942 |
OAT |
ornithine aminotransferase [Source:HGNC ... |
OGDH |
4967 |
OGDH |
oxoglutarate dehydrogenase [Source:HGNC ... |
OPA1 |
4976 |
OPA1 |
OPA1 mitochondrial dynamin like GTPase [... |
OXA1L |
5018 |
OXA1L |
OXA1L mitochondrial inner membrane prote... |
PDHA1 |
5160 |
PDHA1 |
pyruvate dehydrogenase E1 subunit alpha ... |
PDHB |
5162 |
PDHB |
pyruvate dehydrogenase E1 subunit beta [... |
PDHX |
8050 |
PDHX |
pyruvate dehydrogenase complex component... |
PDK4 |
5166 |
PDK4 |
pyruvate dehydrogenase kinase 4 [Source:... |
PDP1 |
54704 |
PDP1 |
pyruvate dehydrogenase phosphatase catal... |
PHB2 |
11331 |
PHB2 |
prohibitin 2 [Source:HGNC Symbol;Acc:HGN... |
PHYH |
5264 |
PHYH |
phytanoyl-CoA 2-hydroxylase [Source:HGNC... |
PMPCA |
23203 |
PMPCA |
peptidase, mitochondrial processing subu... |
POLR2F |
5435 |
POLR2F |
RNA polymerase II, I and III subunit F [... |
POR |
5447 |
POR |
cytochrome p450 oxidoreductase [Source:H... |
PRDX3 |
10935 |
PRDX3 |
peroxiredoxin 3 [Source:HGNC Symbol;Acc:... |
RETSAT |
54884 |
RETSAT |
retinol saturase [Source:HGNC Symbol;Acc... |
RHOT1 |
55288 |
RHOT1 |
ras homolog family member T1 [Source:HGN... |
RHOT2 |
89941 |
RHOT2 |
ras homolog family member T2 [Source:HGN... |
SDHA |
6389 |
SDHA |
succinate dehydrogenase complex flavopro... |
SDHB |
6390 |
SDHB |
succinate dehydrogenase complex iron sul... |
SDHC |
6391 |
SDHC |
succinate dehydrogenase complex subunit ... |
SDHD |
6392 |
SDHD |
succinate dehydrogenase complex subunit ... |
SLC25A11 |
8402 |
SLC25A11 |
solute carrier family 25 member 11 [Sour... |
SLC25A12 |
8604 |
SLC25A12 |
solute carrier family 25 member 12 [Sour... |
SLC25A20 |
788 |
SLC25A20 |
solute carrier family 25 member 20 [Sour... |
SLC25A3 |
5250 |
SLC25A3 |
solute carrier family 25 member 3 [Sourc... |
SLC25A4 |
291 |
SLC25A4 |
solute carrier family 25 member 4 [Sourc... |
SLC25A5 |
292 |
SLC25A5 |
solute carrier family 25 member 5 [Sourc... |
SLC25A6 |
293 |
SLC25A6 |
solute carrier family 25 member 6 [Sourc... |
SUCLA2 |
8803 |
SUCLA2 |
succinate-CoA ligase ADP-forming subunit... |
SUCLG1 |
8802 |
SUCLG1 |
succinate-CoA ligase GDP/ADP-forming sub... |
SUPV3L1 |
6832 |
SUPV3L1 |
Suv3 like RNA helicase [Source:HGNC Symb... |
SURF1 |
6834 |
SURF1 |
SURF1 cytochrome c oxidase assembly fact... |
TCIRG1 |
10312 |
TCIRG1 |
T cell immune regulator 1, ATPase H+ tra... |
TIMM10 |
26519 |
TIMM10 |
translocase of inner mitochondrial membr... |
TIMM13 |
26517 |
TIMM13 |
translocase of inner mitochondrial membr... |
TIMM17A |
10440 |
TIMM17A |
translocase of inner mitochondrial membr... |
TIMM50 |
92609 |
TIMM50 |
translocase of inner mitochondrial membr... |
TIMM8B |
26521 |
TIMM8B |
translocase of inner mitochondrial membr... |
TIMM9 |
26520 |
TIMM9 |
translocase of inner mitochondrial membr... |
TOMM22 |
56993 |
TOMM22 |
translocase of outer mitochondrial membr... |
TOMM70A |
9868 |
TOMM70 |
translocase of outer mitochondrial membr... |
UQCR10 |
29796 |
UQCR10 |
ubiquinol-cytochrome c reductase, comple... |
UQCR11 |
10975 |
UQCR11 |
ubiquinol-cytochrome c reductase, comple... |
UQCRB |
7381 |
UQCRB |
ubiquinol-cytochrome c reductase binding... |
UQCRC1 |
7384 |
UQCRC1 |
ubiquinol-cytochrome c reductase core pr... |
UQCRC2 |
7385 |
UQCRC2 |
ubiquinol-cytochrome c reductase core pr... |
UQCRFS1 |
7386 |
UQCRFS1 |
ubiquinol-cytochrome c reductase, Rieske... |
UQCRH |
7388 |
UQCRH |
ubiquinol-cytochrome c reductase hinge p... |
UQCRQ |
27089 |
UQCRQ |
ubiquinol-cytochrome c reductase complex... |
VDAC1 |
7416 |
VDAC1 |
voltage dependent anion channel 1 [Sourc... |
VDAC2 |
7417 |
VDAC2 |
voltage dependent anion channel 2 [Sourc... |
VDAC3 |
7419 |
VDAC3 |
voltage dependent anion channel 3 [Sourc... |