Source Id |
NCBI (Entrez) Gene Id |
Gene Symbol |
Gene Description |
10105 |
10105 |
PPIF |
peptidylprolyl isomerase F [Source... |
10128 |
10128 |
LRPPRC |
leucine rich pentatricopeptide rep... |
10131 |
10131 |
TRAP1 |
TNF receptor associated protein 1 ... |
10157 |
10157 |
AASS |
aminoadipate-semialdehyde synthase... |
10201 |
10201 |
NME6 |
NME/NM23 nucleoside diphosphate ki... |
10202 |
10202 |
DHRS2 |
dehydrogenase/reductase 2 [Source:... |
10240 |
10240 |
MRPS31 |
mitochondrial ribosomal protein S3... |
10247 |
10247 |
RIDA |
reactive intermediate imine deamin... |
10249 |
10249 |
GLYAT |
glycine-N-acyltransferase [Source:... |
10295 |
10295 |
BCKDK |
branched chain keto acid dehydroge... |
10352 |
10352 |
WARS2 |
tryptophanyl tRNA synthetase 2, mi... |
10449 |
10449 |
ACAA2 |
acetyl-CoA acyltransferase 2 [Sour... |
10456 |
10456 |
HAX1 |
HCLS1 associated protein X-1 [Sour... |
10469 |
10469 |
TIMM44 |
translocase of inner mitochondrial... |
10531 |
10531 |
PITRM1 |
pitrilysin metallopeptidase 1 [Sou... |
10573 |
10573 |
MRPL28 |
mitochondrial ribosomal protein L2... |
10587 |
10587 |
TXNRD2 |
thioredoxin reductase 2 [Source:HG... |
10588 |
10588 |
MTHFS |
methenyltetrahydrofolate synthetas... |
10667 |
10667 |
FARS2 |
phenylalanyl-tRNA synthetase 2, mi... |
10797 |
10797 |
MTHFD2 |
methylenetetrahydrofolate dehydrog... |
10845 |
10845 |
CLPX |
caseinolytic mitochondrial matrix ... |
10873 |
10873 |
ME3 |
malic enzyme 3 [Source:HGNC Symbol... |
10884 |
10884 |
MRPS30 |
mitochondrial ribosomal protein S3... |
10922 |
10922 |
FASTK |
Fas activated serine/threonine kin... |
10935 |
10935 |
PRDX3 |
peroxiredoxin 3 [Source:HGNC Symbo... |
10965 |
10965 |
ACOT2 |
acyl-CoA thioesterase 2 [Source:HG... |
109703458 |
109703458 |
HTD2 |
hydroxyacyl-thioester dehydratase ... |
11019 |
11019 |
LIAS |
lipoic acid synthetase [Source:HGN... |
11112 |
11112 |
HIBADH |
3-hydroxyisobutyrate dehydrogenase... |
11222 |
11222 |
MRPL3 |
mitochondrial ribosomal protein L3... |
11232 |
11232 |
POLG2 |
DNA polymerase gamma 2, accessory ... |
11238 |
11238 |
CA5B |
carbonic anhydrase 5B [Source:HGNC... |
112812 |
112812 |
FDX2 |
ferredoxin 2 [Source:HGNC Symbol;A... |
112817 |
112817 |
HOGA1 |
4-hydroxy-2-oxoglutarate aldolase ... |
11315 |
11315 |
PARK7 |
Parkinsonism associated deglycase ... |
115416 |
115416 |
MALSU1 |
mitochondrial assembly of ribosoma... |
116285 |
116285 |
ACSM1 |
acyl-CoA synthetase medium chain f... |
116447 |
116447 |
TOP1MT |
DNA topoisomerase I mitochondrial ... |
116540 |
116540 |
MRPL53 |
mitochondrial ribosomal protein L5... |
116541 |
116541 |
MRPL54 |
mitochondrial ribosomal protein L5... |
117145 |
117145 |
THEM4 |
thioesterase superfamily member 4 ... |
118487 |
118487 |
CHCHD1 |
coiled-coil-helix-coiled-coil-heli... |
120892 |
120892 |
LRRK2 |
leucine rich repeat kinase 2 [Sour... |
122704 |
122704 |
MRPL52 |
mitochondrial ribosomal protein L5... |
122961 |
122961 |
ISCA2 |
iron-sulfur cluster assembly 2 [So... |
123688 |
123688 |
HYKK |
hydroxylysine kinase [Source:HGNC ... |
123876 |
123876 |
ACSM2A |
acyl-CoA synthetase medium chain f... |
124454 |
124454 |
EARS2 |
glutamyl-tRNA synthetase 2, mitoch... |
124995 |
124995 |
MRPL10 |
mitochondrial ribosomal protein L1... |
128240 |
128240 |
NAXE |
NAD(P)HX epimerase [Source:HGNC Sy... |
128308 |
128308 |
MRPL55 |
mitochondrial ribosomal protein L5... |
130916 |
130916 |
MTERF4 |
mitochondrial transcription termin... |
131118 |
131118 |
DNAJC19 |
DnaJ heat shock protein family (Hs... |
133686 |
133686 |
NADK2 |
NAD kinase 2, mitochondrial [Sourc... |
134266 |
134266 |
GRPEL2 |
GrpE like 2, mitochondrial [Source... |
135154 |
135154 |
SDHAF4 |
succinate dehydrogenase complex as... |
1352 |
1352 |
COX10 |
cytochrome c oxidase assembly fact... |
1373 |
1373 |
CPS1 |
carbamoyl-phosphate synthase 1 [So... |
137872 |
137872 |
ADHFE1 |
alcohol dehydrogenase iron contain... |
140886 |
140886 |
PABPC5 |
poly(A) binding protein cytoplasmi... |
142827 |
142827 |
ACSM6 |
acyl-CoA synthetase medium chain f... |
1431 |
1431 |
CS |
citrate synthase [Source:HGNC Symb... |
152926 |
152926 |
PPM1K |
protein phosphatase, Mg2+/Mn2+ dep... |
1583 |
1583 |
CYP11A1 |
cytochrome P450 family 11 subfamil... |
1593 |
1593 |
CYP27A1 |
cytochrome P450 family 27 subfamil... |
160428 |
160428 |
ALDH1L2 |
aldehyde dehydrogenase 1 family me... |
160760 |
160760 |
PPTC7 |
protein phosphatase targeting COQ7... |
162417 |
162417 |
NAGS |
N-acetylglutamate synthase [Source... |
1629 |
1629 |
DBT |
dihydrolipoamide branched chain tr... |
1632 |
1632 |
ECI1 |
enoyl-CoA delta isomerase 1 [Sourc... |
1666 |
1666 |
DECR1 |
2,4-dienoyl-CoA reductase 1 [Sourc... |
166785 |
166785 |
MMAA |
metabolism of cobalamin associated... |
1716 |
1716 |
DGUOK |
deoxyguanosine kinase [Source:HGNC... |
1737 |
1737 |
DLAT |
dihydrolipoamide S-acetyltransfera... |
1738 |
1738 |
DLD |
dihydrolipoamide dehydrogenase [So... |
1743 |
1743 |
DLST |
dihydrolipoamide S-succinyltransfe... |
1757 |
1757 |
SARDH |
sarcosine dehydrogenase [Source:HG... |
1763 |
1763 |
DNA2 |
DNA replication helicase/nuclease ... |
18 |
18 |
ABAT |
4-aminobutyrate aminotransferase [... |
1841 |
1841 |
DTYMK |
deoxythymidylate kinase [Source:HG... |
1891 |
1891 |
ECH1 |
enoyl-CoA hydratase 1 [Source:HGNC... |
1892 |
1892 |
ECHS1 |
enoyl-CoA hydratase, short chain 1... |
196074 |
196074 |
METTL15 |
methyltransferase 15, mitochondria... |
197322 |
197322 |
ACSF3 |
acyl-CoA synthetase family member ... |
200205 |
200205 |
IBA57 |
iron-sulfur cluster assembly facto... |
200895 |
200895 |
DHFR2 |
dihydrofolate reductase 2 [Source:... |
201626 |
201626 |
PDE12 |
phosphodiesterase 12 [Source:HGNC ... |
201973 |
201973 |
PRIMPOL |
primase and DNA directed polymeras... |
205 |
205 |
AK4 |
adenylate kinase 4 [Source:HGNC Sy... |
205327 |
205327 |
C2orf69 |
chromosome 2 open reading frame 69... |
2066 |
2066 |
ERBB4 |
erb-b2 receptor tyrosine kinase 4 ... |
2108 |
2108 |
ETFA |
electron transfer flavoprotein sub... |
2109 |
2109 |
ETFB |
electron transfer flavoprotein sub... |
211 |
211 |
ALAS1 |
5'-aminolevulinate synthase 1 [Sou... |
2110 |
2110 |
ETFDH |
electron transfer flavoprotein deh... |
212 |
212 |
ALAS2 |
5'-aminolevulinate synthase 2 [Sou... |
217 |
217 |
ALDH2 |
aldehyde dehydrogenase 2 family me... |
219 |
219 |
ALDH1B1 |
aldehyde dehydrogenase 1 family me... |
219927 |
219927 |
MRPL21 |
mitochondrial ribosomal protein L2... |
2230 |
2230 |
FDX1 |
ferredoxin 1 [Source:HGNC Symbol;A... |
2232 |
2232 |
FDXR |
ferredoxin reductase [Source:HGNC ... |
2235 |
2235 |
FECH |
ferrochelatase [Source:HGNC Symbol... |
2271 |
2271 |
FH |
fumarate hydratase [Source:HGNC Sy... |
22868 |
22868 |
FASTKD2 |
FAST kinase domains 2 [Source:HGNC... |
22907 |
22907 |
DHX30 |
DExH-box helicase 30 [Source:HGNC ... |
2309 |
2309 |
FOXO3 |
forkhead box O3 [Source:HGNC Symbo... |
2310 |
2310 |
FOXO3B |
forkhead box O3B [Source:HGNC Symb... |
23107 |
23107 |
MRPS27 |
mitochondrial ribosomal protein S2... |
23203 |
23203 |
PMPCA |
peptidase, mitochondrial processin... |
23395 |
23395 |
LARS2 |
leucyl-tRNA synthetase 2, mitochon... |
23408 |
23408 |
SIRT5 |
sirtuin 5 [Source:HGNC Symbol;Acc:... |
23409 |
23409 |
SIRT4 |
sirtuin 4 [Source:HGNC Symbol;Acc:... |
23410 |
23410 |
SIRT3 |
sirtuin 3 [Source:HGNC Symbol;Acc:... |
23417 |
23417 |
MLYCD |
malonyl-CoA decarboxylase [Source:... |
23438 |
23438 |
HARS2 |
histidyl-tRNA synthetase 2, mitoch... |
23474 |
23474 |
ETHE1 |
ETHE1 persulfide dioxygenase [Sour... |
23479 |
23479 |
ISCU |
iron-sulfur cluster assembly enzym... |
2356 |
2356 |
FPGS |
folylpolyglutamate synthase [Sourc... |
23568 |
23568 |
ARL2BP |
ADP ribosylation factor like GTPas... |
23590 |
23590 |
PDSS1 |
decaprenyl diphosphate synthase su... |
23597 |
23597 |
ACOT9 |
acyl-CoA thioesterase 9 [Source:HG... |
2395 |
2395 |
FXN |
frataxin [Source:HGNC Symbol;Acc:H... |
254013 |
254013 |
ETFBKMT |
electron transfer flavoprotein sub... |
25824 |
25824 |
PRDX5 |
peroxiredoxin 5 [Source:HGNC Symbo... |
25828 |
25828 |
TXN2 |
thioredoxin 2 [Source:HGNC Symbol;... |
25902 |
25902 |
MTHFD1L |
methylenetetrahydrofolate dehydrog... |
25961 |
25961 |
NUDT13 |
nudix hydrolase 13 [Source:HGNC Sy... |
25973 |
25973 |
PARS2 |
prolyl-tRNA synthetase 2, mitochon... |
25996 |
25996 |
REXO2 |
RNA exonuclease 2 [Source:HGNC Sym... |
26024 |
26024 |
PTCD1 |
pentatricopeptide repeat domain 1 ... |
26027 |
26027 |
ACOT11 |
acyl-CoA thioesterase 11 [Source:H... |
26073 |
26073 |
POLDIP2 |
DNA polymerase delta interacting p... |
26164 |
26164 |
MTG2 |
mitochondrial ribosome associated ... |
2617 |
2617 |
GARS1 |
glycyl-tRNA synthetase 1 [Source:H... |
26275 |
26275 |
HIBCH |
3-hydroxyisobutyryl-CoA hydrolase ... |
26284 |
26284 |
ERAL1 |
Era like 12S mitochondrial rRNA ch... |
2631 |
2631 |
NIPSNAP2 |
nipsnap homolog 2 [Source:HGNC Sym... |
2639 |
2639 |
GCDH |
glutaryl-CoA dehydrogenase [Source... |
2647 |
2647 |
BLOC1S1 |
biogenesis of lysosomal organelles... |
2653 |
2653 |
GCSH |
glycine cleavage system protein H ... |
26589 |
26589 |
MRPL46 |
mitochondrial ribosomal protein L4... |
26995 |
26995 |
TRUB2 |
TruB pseudouridine synthase family... |
27034 |
27034 |
ACAD8 |
acyl-CoA dehydrogenase family memb... |
27068 |
27068 |
PPA2 |
inorganic pyrophosphatase 2 [Sourc... |
27165 |
27165 |
GLS2 |
glutaminase 2 [Source:HGNC Symbol;... |
2731 |
2731 |
GLDC |
glycine decarboxylase [Source:HGNC... |
27349 |
27349 |
MCAT |
malonyl-CoA-acyl carrier protein t... |
2744 |
2744 |
GLS |
glutaminase [Source:HGNC Symbol;Ac... |
2746 |
2746 |
GLUD1 |
glutamate dehydrogenase 1 [Source:... |
2747 |
2747 |
GLUD2 |
glutamate dehydrogenase 2 [Source:... |
275 |
275 |
AMT |
aminomethyltransferase [Source:HGN... |
2806 |
2806 |
GOT2 |
glutamic-oxaloacetic transaminase ... |
284486 |
284486 |
THEM5 |
thioesterase superfamily member 5 ... |
285367 |
285367 |
RPUSD3 |
RNA pseudouridine synthase D3 [Sou... |
2876 |
2876 |
GPX1 |
glutathione peroxidase 1 [Source:H... |
28957 |
28957 |
MRPS28 |
mitochondrial ribosomal protein S2... |
28973 |
28973 |
MRPS18B |
mitochondrial ribosomal protein S1... |
28977 |
28977 |
MRPL42 |
mitochondrial ribosomal protein L4... |
28998 |
28998 |
MRPL13 |
mitochondrial ribosomal protein L1... |
29074 |
29074 |
MRPL18 |
mitochondrial ribosomal protein L1... |
2908 |
2908 |
NR3C1 |
nuclear receptor subfamily 3 group... |
29088 |
29088 |
MRPL15 |
mitochondrial ribosomal protein L1... |
29093 |
29093 |
MRPL22 |
mitochondrial ribosomal protein L2... |
29103 |
29103 |
DNAJC15 |
DnaJ heat shock protein family (Hs... |
292 |
292 |
SLC25A5 |
solute carrier family 25 member 5 ... |
2926 |
2926 |
GRSF1 |
G-rich RNA sequence binding factor... |
2936 |
2936 |
GSR |
glutathione-disulfide reductase [S... |
2954 |
2954 |
GSTZ1 |
glutathione S-transferase zeta 1 [... |
29920 |
29920 |
PYCR2 |
pyrroline-5-carboxylate reductase ... |
29958 |
29958 |
DMGDH |
dimethylglycine dehydrogenase [Sou... |
29960 |
29960 |
MRM2 |
mitochondrial rRNA methyltransfera... |
3028 |
3028 |
HSD17B10 |
hydroxysteroid 17-beta dehydrogena... |
3029 |
3029 |
HAGH |
hydroxyacylglutathione hydrolase [... |
3030 |
3030 |
HADHA |
hydroxyacyl-CoA dehydrogenase trif... |
3032 |
3032 |
HADHB |
hydroxyacyl-CoA dehydrogenase trif... |
3033 |
3033 |
HADH |
hydroxyacyl-CoA dehydrogenase [Sou... |
3155 |
3155 |
HMGCL |
3-hydroxy-3-methylglutaryl-CoA lya... |
3158 |
3158 |
HMGCS2 |
3-hydroxy-3-methylglutaryl-CoA syn... |
318 |
318 |
NUDT2 |
nudix hydrolase 2 [Source:HGNC Sym... |
32 |
32 |
ACACB |
acetyl-CoA carboxylase beta [Sourc... |
326625 |
326625 |
MMAB |
metabolism of cobalamin associated... |
33 |
33 |
ACADL |
acyl-CoA dehydrogenase long chain ... |
3305 |
3305 |
HSPA1L |
heat shock protein family A (Hsp70... |
3313 |
3313 |
HSPA9 |
heat shock protein family A (Hsp70... |
3329 |
3329 |
HSPD1 |
heat shock protein family D (Hsp60... |
3336 |
3336 |
HSPE1 |
heat shock protein family E (Hsp10... |
3396 |
3396 |
MRPL58 |
mitochondrial ribosomal protein L5... |
339983 |
339983 |
NAT8L |
N-acetyltransferase 8 like [Source... |
34 |
34 |
ACADM |
acyl-CoA dehydrogenase medium chai... |
341392 |
341392 |
ACSM4 |
acyl-CoA synthetase medium chain f... |
3418 |
3418 |
IDH2 |
isocitrate dehydrogenase (NADP(+))... |
3419 |
3419 |
IDH3A |
isocitrate dehydrogenase (NAD(+)) ... |
3420 |
3420 |
IDH3B |
isocitrate dehydrogenase (NAD(+)) ... |
3421 |
3421 |
IDH3G |
isocitrate dehydrogenase (NAD(+)) ... |
348158 |
348158 |
ACSM2B |
acyl-CoA synthetase medium chain f... |
349565 |
349565 |
NMNAT3 |
nicotinamide nucleotide adenylyltr... |
35 |
35 |
ACADS |
acyl-CoA dehydrogenase short chain... |
36 |
36 |
ACADSB |
acyl-CoA dehydrogenase short/branc... |
37 |
37 |
ACADVL |
acyl-CoA dehydrogenase very long c... |
3712 |
3712 |
IVD |
isovaleryl-CoA dehydrogenase [Sour... |
373156 |
373156 |
GSTK1 |
glutathione S-transferase kappa 1 ... |
3735 |
3735 |
KARS1 |
lysyl-tRNA synthetase 1 [Source:HG... |
374291 |
374291 |
NDUFS7 |
NADH:ubiquinone oxidoreductase cor... |
38 |
38 |
ACAT1 |
acetyl-CoA acetyltransferase 1 [So... |
384 |
384 |
ARG2 |
arginase 2 [Source:HGNC Symbol;Acc... |
387338 |
387338 |
NSUN4 |
NOP2/Sun RNA methyltransferase 4 [... |
387787 |
387787 |
LIPT2 |
lipoyl(octanoyl) transferase 2 [So... |
388962 |
388962 |
BOLA3 |
bolA family member 3 [Source:HGNC ... |
402 |
402 |
ARL2 |
ADP ribosylation factor like GTPas... |
4191 |
4191 |
MDH2 |
malate dehydrogenase 2 [Source:HGN... |
4200 |
4200 |
ME2 |
malic enzyme 2 [Source:HGNC Symbol... |
4285 |
4285 |
MIPEP |
mitochondrial intermediate peptida... |
4287 |
4287 |
ATXN3 |
ataxin 3 [Source:HGNC Symbol;Acc:H... |
4329 |
4329 |
ALDH6A1 |
aldehyde dehydrogenase 6 family me... |
4350 |
4350 |
MPG |
N-methylpurine DNA glycosylase [So... |
4357 |
4357 |
MPST |
mercaptopyruvate sulfurtransferase... |
441024 |
441024 |
MTHFD2L |
methylenetetrahydrofolate dehydrog... |
441282 |
441282 |
AKR1B15 |
aldo-keto reductase family 1 membe... |
4521 |
4521 |
NUDT1 |
nudix hydrolase 1 [Source:HGNC Sym... |
4594 |
4594 |
MMUT |
methylmalonyl-CoA mutase [Source:H... |
4701 |
4701 |
NDUFA7 |
NADH:ubiquinone oxidoreductase sub... |
4704 |
4704 |
NDUFA9 |
NADH:ubiquinone oxidoreductase sub... |
4705 |
4705 |
NDUFA10 |
NADH:ubiquinone oxidoreductase sub... |
4706 |
4706 |
NDUFAB1 |
NADH:ubiquinone oxidoreductase sub... |
4714 |
4714 |
NDUFB8 |
NADH:ubiquinone oxidoreductase sub... |
4719 |
4719 |
NDUFS1 |
NADH:ubiquinone oxidoreductase cor... |
4720 |
4720 |
NDUFS2 |
NADH:ubiquinone oxidoreductase cor... |
4722 |
4722 |
NDUFS3 |
NADH:ubiquinone oxidoreductase cor... |
4728 |
4728 |
NDUFS8 |
NADH:ubiquinone oxidoreductase cor... |
4833 |
4833 |
NME4 |
NME/NM23 nucleoside diphosphate ki... |
4942 |
4942 |
OAT |
ornithine aminotransferase [Source... |
4967 |
4967 |
OGDH |
oxoglutarate dehydrogenase [Source... |
4968 |
4968 |
OGG1 |
8-oxoguanine DNA glycosylase [Sour... |
498 |
498 |
ATP5F1A |
ATP synthase F1 subunit alpha [Sou... |
50 |
50 |
ACO2 |
aconitase 2 [Source:HGNC Symbol;Ac... |
5009 |
5009 |
OTC |
ornithine transcarbamylase [Source... |
501 |
501 |
ALDH7A1 |
aldehyde dehydrogenase 7 family me... |
5018 |
5018 |
OXA1L |
OXA1L mitochondrial inner membrane... |
5019 |
5019 |
OXCT1 |
3-oxoacid CoA-transferase 1 [Sourc... |
506 |
506 |
ATP5F1B |
ATP synthase F1 subunit beta [Sour... |
50808 |
50808 |
AK3 |
adenylate kinase 3 [Source:HGNC Sy... |
509 |
509 |
ATP5F1C |
ATP synthase F1 subunit gamma [Sou... |
5091 |
5091 |
PC |
pyruvate carboxylase [Source:HGNC ... |
5095 |
5095 |
PCCA |
propionyl-CoA carboxylase subunit ... |
5096 |
5096 |
PCCB |
propionyl-CoA carboxylase subunit ... |
51021 |
51021 |
MRPS16 |
mitochondrial ribosomal protein S1... |
51022 |
51022 |
GLRX2 |
glutaredoxin 2 [Source:HGNC Symbol... |
51023 |
51023 |
MRPS18C |
mitochondrial ribosomal protein S1... |
51025 |
51025 |
PAM16 |
presequence translocase associated... |
5106 |
5106 |
PCK2 |
phosphoenolpyruvate carboxykinase ... |
51067 |
51067 |
YARS2 |
tyrosyl-tRNA synthetase 2 [Source:... |
51069 |
51069 |
MRPL2 |
mitochondrial ribosomal protein L2... |
51073 |
51073 |
MRPL4 |
mitochondrial ribosomal protein L4... |
51081 |
51081 |
MRPS7 |
mitochondrial ribosomal protein S7... |
51095 |
51095 |
TRNT1 |
tRNA nucleotidyl transferase 1 [So... |
51102 |
51102 |
MECR |
mitochondrial trans-2-enoyl-CoA re... |
51103 |
51103 |
NDUFAF1 |
NADH:ubiquinone oxidoreductase com... |
51106 |
51106 |
TFB1M |
transcription factor B1, mitochond... |
51110 |
51110 |
LACTB2 |
lactamase beta 2 [Source:HGNC Symb... |
51116 |
51116 |
MRPS2 |
mitochondrial ribosomal protein S2... |
51166 |
51166 |
AADAT |
aminoadipate aminotransferase [Sou... |
51205 |
51205 |
ACP6 |
acid phosphatase 6, lysophosphatid... |
51218 |
51218 |
GLRX5 |
glutaredoxin 5 [Source:HGNC Symbol... |
51250 |
51250 |
MTRES1 |
mitochondrial transcription rescue... |
51253 |
51253 |
MRPL37 |
mitochondrial ribosomal protein L3... |
51258 |
51258 |
MRPL51 |
mitochondrial ribosomal protein L5... |
51263 |
51263 |
MRPL30 |
mitochondrial ribosomal protein L3... |
51264 |
51264 |
MRPL27 |
mitochondrial ribosomal protein L2... |
513 |
513 |
ATP5F1D |
ATP synthase F1 subunit delta [Sou... |
51318 |
51318 |
MRPL35 |
mitochondrial ribosomal protein L3... |
51373 |
51373 |
MRPS17 |
mitochondrial ribosomal protein S1... |
5138 |
5138 |
PDE2A |
phosphodiesterase 2A [Source:HGNC ... |
514 |
514 |
ATP5F1E |
ATP synthase F1 subunit epsilon [S... |
515 |
515 |
ATP5PB |
ATP synthase peripheral stalk-memb... |
5160 |
5160 |
PDHA1 |
pyruvate dehydrogenase E1 subunit ... |
51601 |
51601 |
LIPT1 |
lipoyltransferase 1 [Source:HGNC S... |
5161 |
5161 |
PDHA2 |
pyruvate dehydrogenase E1 subunit ... |
5162 |
5162 |
PDHB |
pyruvate dehydrogenase E1 subunit ... |
5163 |
5163 |
PDK1 |
pyruvate dehydrogenase kinase 1 [S... |
5164 |
5164 |
PDK2 |
pyruvate dehydrogenase kinase 2 [S... |
51642 |
51642 |
MRPL48 |
mitochondrial ribosomal protein L4... |
51649 |
51649 |
MRPS23 |
mitochondrial ribosomal protein S2... |
5165 |
5165 |
PDK3 |
pyruvate dehydrogenase kinase 3 [S... |
51650 |
51650 |
MRPS33 |
mitochondrial ribosomal protein S3... |
51657 |
51657 |
STYXL1 |
serine/threonine/tyrosine interact... |
5166 |
5166 |
PDK4 |
pyruvate dehydrogenase kinase 4 [S... |
51805 |
51805 |
COQ3 |
coenzyme Q3, methyltransferase [So... |
5303 |
5303 |
PIN4 |
peptidylprolyl cis/trans isomerase... |
53343 |
53343 |
NUDT9 |
nudix hydrolase 9 [Source:HGNC Sym... |
54148 |
54148 |
MRPL39 |
mitochondrial ribosomal protein L3... |
5428 |
5428 |
POLG |
DNA polymerase gamma, catalytic su... |
5442 |
5442 |
POLRMT |
RNA polymerase mitochondrial [Sour... |
54460 |
54460 |
MRPS21 |
mitochondrial ribosomal protein S2... |
54516 |
54516 |
MTRF1L |
mitochondrial translation release ... |
54534 |
54534 |
MRPL50 |
mitochondrial ribosomal protein L5... |
54704 |
54704 |
PDP1 |
pyruvate dehydrogenase phosphatase... |
54802 |
54802 |
TRIT1 |
tRNA isopentenyltransferase 1 [Sou... |
549 |
549 |
AUH |
AU RNA binding methylglutaconyl-Co... |
54931 |
54931 |
TRMT10C |
tRNA methyltransferase 10C, mitoch... |
54936 |
54936 |
ADPRS |
ADP-ribosylserine hydrolase [Sourc... |
54938 |
54938 |
SARS2 |
seryl-tRNA synthetase 2, mitochond... |
54948 |
54948 |
MRPL16 |
mitochondrial ribosomal protein L1... |
54949 |
54949 |
SDHAF2 |
succinate dehydrogenase complex as... |
54988 |
54988 |
ACSM5 |
acyl-CoA synthetase medium chain f... |
54995 |
54995 |
OXSM |
3-oxoacyl-ACP synthase, mitochondr... |
54998 |
54998 |
AURKAIP1 |
aurora kinase A interacting protei... |
55006 |
55006 |
TRMT61B |
tRNA methyltransferase 61B [Source... |
55028 |
55028 |
C17orf80 |
chromosome 17 open reading frame 8... |
55037 |
55037 |
PTCD3 |
pentatricopeptide repeat domain 3 ... |
55052 |
55052 |
MRPL20 |
mitochondrial ribosomal protein L2... |
55066 |
55066 |
PDPR |
pyruvate dehydrogenase phosphatase... |
55157 |
55157 |
DARS2 |
aspartyl-tRNA synthetase 2, mitoch... |
55168 |
55168 |
MRPS18A |
mitochondrial ribosomal protein S1... |
55173 |
55173 |
MRPS10 |
mitochondrial ribosomal protein S1... |
55178 |
55178 |
MRM3 |
mitochondrial rRNA methyltransfera... |
55210 |
55210 |
ATAD3A |
ATPase family AAA domain containin... |
55217 |
55217 |
TMLHE |
trimethyllysine hydroxylase, epsil... |
55218 |
55218 |
EXD2 |
exonuclease 3'-5' domain containin... |
55347 |
55347 |
ABHD10 |
abhydrolase domain containing 10, ... |
55379 |
55379 |
LRRC59 |
leucine rich repeat containing 59 ... |
55471 |
55471 |
NDUFAF7 |
NADH:ubiquinone oxidoreductase com... |
55526 |
55526 |
DHTKD1 |
dehydrogenase E1 and transketolase... |
5566 |
5566 |
PRKACA |
protein kinase cAMP-activated cata... |
55699 |
55699 |
IARS2 |
isoleucyl-tRNA synthetase 2, mitoc... |
55739 |
55739 |
NAXD |
NAD(P)HX dehydratase [Source:HGNC ... |
55753 |
55753 |
OGDHL |
oxoglutarate dehydrogenase L [Sour... |
55794 |
55794 |
DDX28 |
DEAD-box helicase 28 [Source:HGNC ... |
55856 |
55856 |
ACOT13 |
acyl-CoA thioesterase 13 [Source:H... |
55902 |
55902 |
ACSS2 |
acyl-CoA synthetase short chain fa... |
5625 |
5625 |
PRODH |
proline dehydrogenase 1 [Source:HG... |
56652 |
56652 |
TWNK |
twinkle mtDNA helicase [Source:HGN... |
56922 |
56922 |
MCCC1 |
methylcrotonyl-CoA carboxylase sub... |
56945 |
56945 |
MRPS22 |
mitochondrial ribosomal protein S2... |
56953 |
56953 |
NT5M |
5',3'-nucleotidase, mitochondrial ... |
57001 |
57001 |
SDHAF3 |
succinate dehydrogenase complex as... |
57038 |
57038 |
RARS2 |
arginyl-tRNA synthetase 2, mitocho... |
57107 |
57107 |
PDSS2 |
decaprenyl diphosphate synthase su... |
57128 |
57128 |
LYRM4 |
LYR motif containing 4 [Source:HGN... |
57129 |
57129 |
MRPL47 |
mitochondrial ribosomal protein L4... |
57546 |
57546 |
PDP2 |
pyruvate dehydrogenase phosphatase... |
57570 |
57570 |
TRMT5 |
tRNA methyltransferase 5 [Source:H... |
5770 |
5770 |
PTPN1 |
protein tyrosine phosphatase non-r... |
57805 |
57805 |
CCAR2 |
cell cycle and apoptosis regulator... |
58157 |
58157 |
NGB |
neuroglobin [Source:HGNC Symbol;Ac... |
5831 |
5831 |
PYCR1 |
pyrroline-5-carboxylate reductase ... |
5859 |
5859 |
QARS1 |
glutaminyl-tRNA synthetase 1 [Sour... |
587 |
587 |
BCAT2 |
branched chain amino acid transami... |
5888 |
5888 |
RAD51 |
RAD51 recombinase [Source:HGNC Sym... |
593 |
593 |
BCKDHA |
branched chain keto acid dehydroge... |
594 |
594 |
BCKDHB |
branched chain keto acid dehydroge... |
598 |
598 |
BCL2L1 |
BCL2 like 1 [Source:HGNC Symbol;Ac... |
60314 |
60314 |
MYG1 |
MYG1 exonuclease [Source:HGNC Symb... |
6041 |
6041 |
RNASEL |
ribonuclease L [Source:HGNC Symbol... |
60488 |
60488 |
MRPS35 |
mitochondrial ribosomal protein S3... |
60493 |
60493 |
FASTKD5 |
FAST kinase domains 5 [Source:HGNC... |
60528 |
60528 |
ELAC2 |
elaC ribonuclease Z 2 [Source:HGNC... |
60558 |
60558 |
GUF1 |
GTP binding elongation factor GUF1... |
6059 |
6059 |
ABCE1 |
ATP binding cassette subfamily E m... |
6150 |
6150 |
MRPL23 |
mitochondrial ribosomal protein L2... |
6182 |
6182 |
MRPL12 |
mitochondrial ribosomal protein L1... |
6183 |
6183 |
MRPS12 |
mitochondrial ribosomal protein S1... |
6188 |
6188 |
RPS3 |
ribosomal protein S3 [Source:HGNC ... |
622 |
622 |
BDH1 |
3-hydroxybutyrate dehydrogenase 1 ... |
6296 |
6296 |
ACSM3 |
acyl-CoA synthetase medium chain f... |
63875 |
63875 |
MRPL17 |
mitochondrial ribosomal protein L1... |
63899 |
63899 |
NSUN3 |
NOP2/Sun RNA methyltransferase 3 [... |
63904 |
63904 |
DUSP21 |
dual specificity phosphatase 21 [S... |
63931 |
63931 |
MRPS14 |
mitochondrial ribosomal protein S1... |
63970 |
63970 |
TP53AIP1 |
tumor protein p53 regulated apopto... |
64064 |
64064 |
OXCT2 |
3-oxoacid CoA-transferase 2 [Sourc... |
64087 |
64087 |
MCCC2 |
methylcrotonyl-CoA carboxylase sub... |
64216 |
64216 |
TFB2M |
transcription factor B2, mitochond... |
644096 |
644096 |
SDHAF1 |
succinate dehydrogenase complex as... |
64432 |
64432 |
MRPS25 |
mitochondrial ribosomal protein S2... |
6464 |
6464 |
SHC1 |
SHC adaptor protein 1 [Source:HGNC... |
6472 |
6472 |
SHMT2 |
serine hydroxymethyltransferase 2 ... |
64745 |
64745 |
METTL17 |
methyltransferase like 17 [Source:... |
64850 |
64850 |
ETNPPL |
ethanolamine-phosphate phospho-lya... |
64863 |
64863 |
METTL4 |
methyltransferase 4, N6-adenosine ... |
64902 |
64902 |
AGXT2 |
alanine--glyoxylate aminotransfera... |
64928 |
64928 |
MRPL14 |
mitochondrial ribosomal protein L1... |
64949 |
64949 |
MRPS26 |
mitochondrial ribosomal protein S2... |
64951 |
64951 |
MRPS24 |
mitochondrial ribosomal protein S2... |
64960 |
64960 |
MRPS15 |
mitochondrial ribosomal protein S1... |
64963 |
64963 |
MRPS11 |
mitochondrial ribosomal protein S1... |
64965 |
64965 |
MRPS9 |
mitochondrial ribosomal protein S9... |
64968 |
64968 |
MRPS6 |
mitochondrial ribosomal protein S6... |
64969 |
64969 |
MRPS5 |
mitochondrial ribosomal protein S5... |
64975 |
64975 |
MRPL41 |
mitochondrial ribosomal protein L4... |
64976 |
64976 |
MRPL40 |
mitochondrial ribosomal protein L4... |
64978 |
64978 |
MRPL38 |
mitochondrial ribosomal protein L3... |
64979 |
64979 |
MRPL36 |
mitochondrial ribosomal protein L3... |
64981 |
64981 |
MRPL34 |
mitochondrial ribosomal protein L3... |
64983 |
64983 |
MRPL32 |
mitochondrial ribosomal protein L3... |
65003 |
65003 |
MRPL11 |
mitochondrial ribosomal protein L1... |
65005 |
65005 |
MRPL9 |
mitochondrial ribosomal protein L9... |
65008 |
65008 |
MRPL1 |
mitochondrial ribosomal protein L1... |
65080 |
65080 |
MRPL44 |
mitochondrial ribosomal protein L4... |
65993 |
65993 |
MRPS34 |
mitochondrial ribosomal protein S3... |
6647 |
6647 |
SOD1 |
superoxide dismutase 1 [Source:HGN... |
6648 |
6648 |
SOD2 |
superoxide dismutase 2 [Source:HGN... |
6742 |
6742 |
SSBP1 |
single stranded DNA binding protei... |
6770 |
6770 |
STAR |
steroidogenic acute regulatory pro... |
6821 |
6821 |
SUOX |
sulfite oxidase [Source:HGNC Symbo... |
6832 |
6832 |
SUPV3L1 |
Suv3 like RNA helicase [Source:HGN... |
686 |
686 |
BTD |
biotinidase [Source:HGNC Symbol;Ac... |
7015 |
7015 |
TERT |
telomerase reverse transcriptase [... |
7019 |
7019 |
TFAM |
transcription factor A, mitochondr... |
708 |
708 |
C1QBP |
complement C1q binding protein [So... |
7084 |
7084 |
TK2 |
thymidine kinase 2 [Source:HGNC Sy... |
7156 |
7156 |
TOP3A |
DNA topoisomerase III alpha [Sourc... |
7157 |
7157 |
TP53 |
tumor protein p53 [Source:HGNC Sym... |
7263 |
7263 |
TST |
thiosulfate sulfurtransferase [Sou... |
728294 |
728294 |
D2HGDH |
D-2-hydroxyglutarate dehydrogenase... |
7284 |
7284 |
TUFM |
Tu translation elongation factor, ... |
7298 |
7298 |
TYMS |
thymidylate synthetase [Source:HGN... |
740 |
740 |
MRPL49 |
mitochondrial ribosomal protein L4... |
7416 |
7416 |
VDAC1 |
voltage dependent anion channel 1 ... |
7417 |
7417 |
VDAC2 |
voltage dependent anion channel 2 ... |
763 |
763 |
CA5A |
carbonic anhydrase 5A [Source:HGNC... |
7818 |
7818 |
DAP3 |
death associated protein 3 [Source... |
78988 |
78988 |
MRPL57 |
mitochondrial ribosomal protein L5... |
79072 |
79072 |
FASTKD3 |
FAST kinase domains 3 [Source:HGNC... |
7915 |
7915 |
ALDH5A1 |
aldehyde dehydrogenase 5 family me... |
7923 |
7923 |
HSD17B8 |
hydroxysteroid 17-beta dehydrogena... |
79568 |
79568 |
MAIP1 |
matrix AAA peptidase interacting p... |
79586 |
79586 |
CHPF |
chondroitin polymerizing factor [S... |
79590 |
79590 |
MRPL24 |
mitochondrial ribosomal protein L2... |
79611 |
79611 |
ACSS3 |
acyl-CoA synthetase short chain fa... |
79675 |
79675 |
FASTKD1 |
FAST kinase domains 1 [Source:HGNC... |
79731 |
79731 |
NARS2 |
asparaginyl-tRNA synthetase 2, mit... |
79736 |
79736 |
TEFM |
transcription elongation factor, m... |
7978 |
7978 |
MTERF1 |
mitochondrial transcription termin... |
79922 |
79922 |
MRM1 |
mitochondrial rRNA methyltransfera... |
79979 |
79979 |
TRMT2B |
tRNA methyltransferase 2 homolog B... |
80017 |
80017 |
DGLUCY |
D-glutamate cyclase [Source:HGNC S... |
80221 |
80221 |
ACSF2 |
acyl-CoA synthetase family member ... |
80222 |
80222 |
TARS2 |
threonyl-tRNA synthetase 2, mitoch... |
80224 |
80224 |
NUBPL |
NUBP iron-sulfur cluster assembly ... |
80273 |
80273 |
GRPEL1 |
GrpE like 1, mitochondrial [Source... |
80298 |
80298 |
MTERF2 |
mitochondrial transcription termin... |
80308 |
80308 |
FLAD1 |
flavin adenine dinucleotide synthe... |
80324 |
80324 |
PUS1 |
pseudouridine synthase 1 [Source:H... |
80347 |
80347 |
COASY |
Coenzyme A synthase [Source:HGNC S... |
8050 |
8050 |
PDHX |
pyruvate dehydrogenase complex com... |
80724 |
80724 |
ACAD10 |
acyl-CoA dehydrogenase family memb... |
81689 |
81689 |
ISCA1 |
iron-sulfur cluster assembly 1 [So... |
81889 |
81889 |
FAHD1 |
fumarylacetoacetate hydrolase doma... |
81892 |
81892 |
SLIRP |
SRA stem-loop interacting RNA bind... |
8192 |
8192 |
CLPP |
caseinolytic mitochondrial matrix ... |
83451 |
83451 |
ABHD11 |
abhydrolase domain containing 11 [... |
83875 |
83875 |
BCO2 |
beta-carotene oxygenase 2 [Source:... |
84266 |
84266 |
ALKBH7 |
alkB homolog 7 [Source:HGNC Symbol... |
84274 |
84274 |
COQ5 |
coenzyme Q5, methyltransferase [So... |
84300 |
84300 |
UQCC2 |
ubiquinol-cytochrome c reductase c... |
84311 |
84311 |
MRPL45 |
mitochondrial ribosomal protein L4... |
84340 |
84340 |
GFM2 |
GTP dependent ribosome recycling f... |
844 |
844 |
CASQ1 |
calsequestrin 1 [Source:HGNC Symbo... |
84532 |
84532 |
ACSS1 |
acyl-CoA synthetase short chain fa... |
84545 |
84545 |
MRPL43 |
mitochondrial ribosomal protein L4... |
84693 |
84693 |
MCEE |
methylmalonyl-CoA epimerase [Sourc... |
84706 |
84706 |
GPT2 |
glutamic--pyruvic transaminase 2 [... |
84769 |
84769 |
MPV17L2 |
MPV17 mitochondrial inner membrane... |
84795 |
84795 |
PYROXD2 |
pyridine nucleotide-disulphide oxi... |
84816 |
84816 |
RTN4IP1 |
reticulon 4 interacting protein 1 ... |
84869 |
84869 |
CBR4 |
carbonyl reductase 4 [Source:HGNC ... |
84881 |
84881 |
RPUSD4 |
RNA pseudouridine synthase D4 [Sou... |
84971 |
84971 |
ATG4D |
autophagy related 4D cysteine pept... |
85007 |
85007 |
PHYKPL |
5-phosphohydroxy-L-lysine phospho-... |
8505 |
8505 |
PARG |
poly(ADP-ribose) glycohydrolase [S... |
8508 |
8508 |
NIPSNAP1 |
nipsnap homolog 1 [Source:HGNC Sym... |
85476 |
85476 |
GFM1 |
G elongation factor mitochondrial ... |
8659 |
8659 |
ALDH4A1 |
aldehyde dehydrogenase 4 family me... |
87178 |
87178 |
PNPT1 |
polyribonucleotide nucleotidyltran... |
8801 |
8801 |
SUCLG2 |
succinate-CoA ligase GDP-forming s... |
8802 |
8802 |
SUCLG1 |
succinate-CoA ligase GDP/ADP-formi... |
8803 |
8803 |
SUCLA2 |
succinate-CoA ligase ADP-forming s... |
891 |
891 |
CCNB1 |
cyclin B1 [Source:HGNC Symbol;Acc:... |
89839 |
89839 |
ARHGAP11B |
Rho GTPase activating protein 11B ... |
90480 |
90480 |
GADD45GIP1 |
GADD45G interacting protein 1 [Sou... |
9054 |
9054 |
NFS1 |
NFS1 cysteine desulfurase [Source:... |
90624 |
90624 |
LYRM7 |
LYR motif containing 7 [Source:HGN... |
9093 |
9093 |
DNAJA3 |
DnaJ heat shock protein family (Hs... |
91689 |
91689 |
SMDT1 |
single-pass membrane protein with ... |
91875 |
91875 |
TTC5 |
tetratricopeptide repeat domain 5 ... |
92170 |
92170 |
MTG1 |
mitochondrial ribosome associated ... |
9238 |
9238 |
TBRG4 |
transforming growth factor beta re... |
92399 |
92399 |
MRRF |
mitochondrial ribosome recycling f... |
92483 |
92483 |
LDHAL6B |
lactate dehydrogenase A like 6B [S... |
92935 |
92935 |
MARS2 |
methionyl-tRNA synthetase 2, mitoc... |
9361 |
9361 |
LONP1 |
lon peptidase 1, mitochondrial [So... |
94033 |
94033 |
FTMT |
ferritin mitochondrial [Source:HGN... |
9512 |
9512 |
PMPCB |
peptidase, mitochondrial processin... |
9553 |
9553 |
MRPL33 |
mitochondrial ribosomal protein L3... |
9692 |
9692 |
PRORP |
protein only RNase P catalytic sub... |
9801 |
9801 |
MRPL19 |
mitochondrial ribosomal protein L1... |
983 |
983 |
CDK1 |
cyclin dependent kinase 1 [Source:... |
9997 |
9997 |
SCO2 |
synthesis of cytochrome C oxidase ... |