Source Id |
NCBI (Entrez) Gene Id |
Gene Symbol |
Gene Description |
100128525 |
100128525 |
UQCRFS1P1 |
ubiquinol-cytochrome c reductas... |
100532726 |
100532726 |
NDUFC2-KCTD14 |
NDUFC2-KCTD14 readthrough [Sour... |
10105 |
10105 |
PPIF |
peptidylprolyl isomerase F [Sou... |
10476 |
10476 |
ATP5PD |
ATP synthase peripheral stalk s... |
10632 |
10632 |
ATP5MG |
ATP synthase membrane subunit g... |
107075310 |
107075310 |
MTCO2P12 |
MT-CO2 pseudogene 12 [Source:HG... |
10873 |
10873 |
ME3 |
malic enzyme 3 [Source:HGNC Sym... |
10975 |
10975 |
UQCR11 |
ubiquinol-cytochrome c reductas... |
113115 |
113115 |
MTFR2 |
mitochondrial fission regulator... |
11315 |
11315 |
PARK7 |
Parkinsonism associated deglyca... |
125965 |
125965 |
COX6B2 |
cytochrome c oxidase subunit 6B... |
126328 |
126328 |
NDUFA11 |
NADH:ubiquinone oxidoreductase ... |
1291 |
1291 |
COL6A1 |
collagen type VI alpha 1 chain ... |
130752 |
130752 |
MDH1B |
malate dehydrogenase 1B [Source... |
1327 |
1327 |
COX4I1 |
cytochrome c oxidase subunit 4I... |
1329 |
1329 |
COX5B |
cytochrome c oxidase subunit 5B... |
1337 |
1337 |
COX6A1 |
cytochrome c oxidase subunit 6A... |
1339 |
1339 |
COX6A2 |
cytochrome c oxidase subunit 6A... |
1340 |
1340 |
COX6B1 |
cytochrome c oxidase subunit 6B... |
134145 |
134145 |
ATPSCKMT |
ATP synthase c subunit lysine N... |
1345 |
1345 |
COX6C |
cytochrome c oxidase subunit 6C... |
1346 |
1346 |
COX7A1 |
cytochrome c oxidase subunit 7A... |
1347 |
1347 |
COX7A2 |
cytochrome c oxidase subunit 7A... |
1348 |
1348 |
COX7A2P2 |
cytochrome c oxidase subunit 7A... |
1349 |
1349 |
COX7B |
cytochrome c oxidase subunit 7B... |
1350 |
1350 |
COX7C |
cytochrome c oxidase subunit 7C... |
1351 |
1351 |
COX8A |
cytochrome c oxidase subunit 8A... |
1352 |
1352 |
COX10 |
cytochrome c oxidase assembly f... |
1431 |
1431 |
CS |
citrate synthase [Source:HGNC S... |
1537 |
1537 |
CYC1 |
cytochrome c1 [Source:HGNC Symb... |
158 |
158 |
ADSL |
adenylosuccinate lyase [Source:... |
170712 |
170712 |
COX7B2 |
cytochrome c oxidase subunit 7B... |
1716 |
1716 |
DGUOK |
deoxyguanosine kinase [Source:H... |
1737 |
1737 |
DLAT |
dihydrolipoamide S-acetyltransf... |
1738 |
1738 |
DLD |
dihydrolipoamide dehydrogenase ... |
1743 |
1743 |
DLST |
dihydrolipoamide S-succinyltran... |
205 |
205 |
AK4 |
adenylate kinase 4 [Source:HGNC... |
205327 |
205327 |
C2orf69 |
chromosome 2 open reading frame... |
215 |
215 |
ABCD1 |
ATP binding cassette subfamily ... |
2271 |
2271 |
FH |
fumarate hydratase [Source:HGNC... |
23410 |
23410 |
SIRT3 |
sirtuin 3 [Source:HGNC Symbol;A... |
23479 |
23479 |
ISCU |
iron-sulfur cluster assembly en... |
23530 |
23530 |
NNT |
nicotinamide nucleotide transhy... |
2395 |
2395 |
FXN |
frataxin [Source:HGNC Symbol;Ac... |
246269 |
246269 |
AFG1L |
AFG1 like ATPase [Source:HGNC S... |
2631 |
2631 |
NIPSNAP2 |
nipsnap homolog 2 [Source:HGNC ... |
2647 |
2647 |
BLOC1S1 |
biogenesis of lysosomal organel... |
26471 |
26471 |
NUPR1 |
nuclear protein 1, transcriptio... |
27069 |
27069 |
GHITM |
growth hormone inducible transm... |
27089 |
27089 |
UQCRQ |
ubiquinol-cytochrome c reductas... |
29103 |
29103 |
DNAJC15 |
DnaJ heat shock protein family ... |
29796 |
29796 |
UQCR10 |
ubiquinol-cytochrome c reductas... |
29997 |
29997 |
NOP53 |
NOP53 ribosome biogenesis facto... |
3091 |
3091 |
HIF1A |
hypoxia inducible factor 1 subu... |
30968 |
30968 |
STOML2 |
stomatin like 2 [Source:HGNC Sy... |
3416 |
3416 |
IDE |
insulin degrading enzyme [Sourc... |
3417 |
3417 |
IDH1 |
isocitrate dehydrogenase (NADP(... |
3418 |
3418 |
IDH2 |
isocitrate dehydrogenase (NADP(... |
3419 |
3419 |
IDH3A |
isocitrate dehydrogenase (NAD(+... |
341947 |
341947 |
COX8C |
cytochrome c oxidase subunit 8C... |
3420 |
3420 |
IDH3B |
isocitrate dehydrogenase (NAD(+... |
3421 |
3421 |
IDH3G |
isocitrate dehydrogenase (NAD(+... |
3658 |
3658 |
IREB2 |
iron responsive element binding... |
374291 |
374291 |
NDUFS7 |
NADH:ubiquinone oxidoreductase ... |
387 |
387 |
RHOA |
ras homolog family member A [So... |
388753 |
388753 |
COA6 |
cytochrome c oxidase assembly f... |
400916 |
400916 |
CHCHD10 |
coiled-coil-helix-coiled-coil-h... |
402 |
402 |
ARL2 |
ADP ribosylation factor like GT... |
406992 |
406992 |
MIR210 |
microRNA 210 [Source:HGNC Symbo... |
4190 |
4190 |
MDH1 |
malate dehydrogenase 1 [Source:... |
4191 |
4191 |
MDH2 |
malate dehydrogenase 2 [Source:... |
432369 |
432369 |
ATP5F1EP2 |
ATP synthase F1 subunit epsilon... |
440567 |
440567 |
UQCRHL |
ubiquinol-cytochrome c reductas... |
4436 |
4436 |
MSH2 |
mutS homolog 2 [Source:HGNC Sym... |
4508 |
4508 |
MT-ATP6 |
mitochondrially encoded ATP syn... |
4509 |
4509 |
MT-ATP8 |
mitochondrially encoded ATP syn... |
4512 |
4512 |
MT-CO1 |
mitochondrially encoded cytochr... |
4513 |
4513 |
MT-CO2 |
mitochondrially encoded cytochr... |
4514 |
4514 |
MT-CO3 |
mitochondrially encoded cytochr... |
4519 |
4519 |
MT-CYB |
mitochondrially encoded cytochr... |
4535 |
4535 |
MT-ND1 |
mitochondrially encoded NADH:ub... |
4536 |
4536 |
MT-ND2 |
mitochondrially encoded NADH:ub... |
4537 |
4537 |
MT-ND3 |
mitochondrially encoded NADH:ub... |
4538 |
4538 |
MT-ND4 |
mitochondrially encoded NADH:ub... |
4539 |
4539 |
MT-ND4L |
mitochondrially encoded NADH:ub... |
4540 |
4540 |
MT-ND5 |
mitochondrially encoded NADH:ub... |
4541 |
4541 |
MT-ND6 |
mitochondrially encoded NADH:ub... |
4693 |
4693 |
NDP |
norrin cystine knot growth fact... |
4694 |
4694 |
NDUFA1 |
NADH:ubiquinone oxidoreductase ... |
4695 |
4695 |
NDUFA2 |
NADH:ubiquinone oxidoreductase ... |
4696 |
4696 |
NDUFA3 |
NADH:ubiquinone oxidoreductase ... |
4697 |
4697 |
NDUFA4 |
NDUFA4 mitochondrial complex as... |
4698 |
4698 |
NDUFA5 |
NADH:ubiquinone oxidoreductase ... |
4700 |
4700 |
NDUFA6 |
NADH:ubiquinone oxidoreductase ... |
4701 |
4701 |
NDUFA7 |
NADH:ubiquinone oxidoreductase ... |
4702 |
4702 |
NDUFA8 |
NADH:ubiquinone oxidoreductase ... |
4704 |
4704 |
NDUFA9 |
NADH:ubiquinone oxidoreductase ... |
4705 |
4705 |
NDUFA10 |
NADH:ubiquinone oxidoreductase ... |
4706 |
4706 |
NDUFAB1 |
NADH:ubiquinone oxidoreductase ... |
4707 |
4707 |
NDUFB1 |
NADH:ubiquinone oxidoreductase ... |
4708 |
4708 |
NDUFB2 |
NADH:ubiquinone oxidoreductase ... |
4709 |
4709 |
NDUFB3 |
NADH:ubiquinone oxidoreductase ... |
4710 |
4710 |
NDUFB4 |
NADH:ubiquinone oxidoreductase ... |
4711 |
4711 |
NDUFB5 |
NADH:ubiquinone oxidoreductase ... |
4712 |
4712 |
NDUFB6 |
NADH:ubiquinone oxidoreductase ... |
4713 |
4713 |
NDUFB7 |
NADH:ubiquinone oxidoreductase ... |
4714 |
4714 |
NDUFB8 |
NADH:ubiquinone oxidoreductase ... |
4715 |
4715 |
NDUFB9 |
NADH:ubiquinone oxidoreductase ... |
4716 |
4716 |
NDUFB10 |
NADH:ubiquinone oxidoreductase ... |
4717 |
4717 |
NDUFC1 |
NADH:ubiquinone oxidoreductase ... |
4718 |
4718 |
NDUFC2 |
NADH:ubiquinone oxidoreductase ... |
4719 |
4719 |
NDUFS1 |
NADH:ubiquinone oxidoreductase ... |
4720 |
4720 |
NDUFS2 |
NADH:ubiquinone oxidoreductase ... |
4722 |
4722 |
NDUFS3 |
NADH:ubiquinone oxidoreductase ... |
4723 |
4723 |
NDUFV1 |
NADH:ubiquinone oxidoreductase ... |
4724 |
4724 |
NDUFS4 |
NADH:ubiquinone oxidoreductase ... |
4725 |
4725 |
NDUFS5 |
NADH:ubiquinone oxidoreductase ... |
4726 |
4726 |
NDUFS6 |
NADH:ubiquinone oxidoreductase ... |
4728 |
4728 |
NDUFS8 |
NADH:ubiquinone oxidoreductase ... |
4729 |
4729 |
NDUFV2 |
NADH:ubiquinone oxidoreductase ... |
4731 |
4731 |
NDUFV3 |
NADH:ubiquinone oxidoreductase ... |
48 |
48 |
ACO1 |
aconitase 1 [Source:HGNC Symbol... |
4967 |
4967 |
OGDH |
oxoglutarate dehydrogenase [Sou... |
498 |
498 |
ATP5F1A |
ATP synthase F1 subunit alpha [... |
50 |
50 |
ACO2 |
aconitase 2 [Source:HGNC Symbol... |
5018 |
5018 |
OXA1L |
OXA1L mitochondrial inner membr... |
506 |
506 |
ATP5F1B |
ATP synthase F1 subunit beta [S... |
509 |
509 |
ATP5F1C |
ATP synthase F1 subunit gamma [... |
51079 |
51079 |
NDUFA13 |
NADH:ubiquinone oxidoreductase ... |
51085 |
51085 |
MLXIPL |
MLX interacting protein like [S... |
51103 |
51103 |
NDUFAF1 |
NADH:ubiquinone oxidoreductase ... |
51142 |
51142 |
CHCHD2 |
coiled-coil-helix-coiled-coil-h... |
513 |
513 |
ATP5F1D |
ATP synthase F1 subunit delta [... |
514 |
514 |
ATP5F1E |
ATP synthase F1 subunit epsilon... |
515 |
515 |
ATP5PB |
ATP synthase peripheral stalk-m... |
5160 |
5160 |
PDHA1 |
pyruvate dehydrogenase E1 subun... |
5161 |
5161 |
PDHA2 |
pyruvate dehydrogenase E1 subun... |
5162 |
5162 |
PDHB |
pyruvate dehydrogenase E1 subun... |
521 |
521 |
ATP5ME |
ATP synthase membrane subunit e... |
522 |
522 |
ATP5PF |
ATP synthase peripheral stalk s... |
538 |
538 |
ATP7A |
ATPase copper transporting alph... |
539 |
539 |
ATP5PO |
ATP synthase peripheral stalk s... |
54205 |
54205 |
CYCS |
cytochrome c, somatic [Source:H... |
54539 |
54539 |
NDUFB11 |
NADH:ubiquinone oxidoreductase ... |
54949 |
54949 |
SDHAF2 |
succinate dehydrogenase complex... |
55753 |
55753 |
OGDHL |
oxoglutarate dehydrogenase L [S... |
55967 |
55967 |
NDUFA12 |
NADH:ubiquinone oxidoreductase ... |
56181 |
56181 |
MTFR1L |
mitochondrial fission regulator... |
57017 |
57017 |
COQ9 |
coenzyme Q9 [Source:HGNC Symbol... |
59341 |
59341 |
TRPV4 |
transient receptor potential ca... |
637 |
637 |
BID |
BH3 interacting domain death ag... |
6389 |
6389 |
SDHA |
succinate dehydrogenase complex... |
6390 |
6390 |
SDHB |
succinate dehydrogenase complex... |
6391 |
6391 |
SDHC |
succinate dehydrogenase complex... |
6392 |
6392 |
SDHD |
succinate dehydrogenase complex... |
6472 |
6472 |
SHMT2 |
serine hydroxymethyltransferase... |
65018 |
65018 |
PINK1 |
PTEN induced kinase 1 [Source:H... |
65084 |
65084 |
TMEM135 |
transmembrane protein 135 [Sour... |
65990 |
65990 |
ANTKMT |
adenine nucleotide translocase ... |
6622 |
6622 |
SNCA |
synuclein alpha [Source:HGNC Sy... |
664 |
664 |
BNIP3 |
BCL2 interacting protein 3 [Sou... |
6834 |
6834 |
SURF1 |
SURF1 cytochrome c oxidase asse... |
6901 |
6901 |
TAFAZZIN |
tafazzin, phospholipid-lysophos... |
7124 |
7124 |
TNF |
tumor necrosis factor [Source:H... |
7349 |
7349 |
UCN |
urocortin [Source:HGNC Symbol;A... |
7381 |
7381 |
UQCRB |
ubiquinol-cytochrome c reductas... |
7384 |
7384 |
UQCRC1 |
ubiquinol-cytochrome c reductas... |
7385 |
7385 |
UQCRC2 |
ubiquinol-cytochrome c reductas... |
7386 |
7386 |
UQCRFS1 |
ubiquinol-cytochrome c reductas... |
7388 |
7388 |
UQCRH |
ubiquinol-cytochrome c reductas... |
7415 |
7415 |
VCP |
valosin containing protein [Sou... |
79085 |
79085 |
SLC25A23 |
solute carrier family 25 member... |
790955 |
790955 |
UQCC3 |
ubiquinol-cytochrome c reductas... |
79736 |
79736 |
TEFM |
transcription elongation factor... |
80025 |
80025 |
PANK2 |
pantothenate kinase 2 [Source:H... |
84275 |
84275 |
SLC25A33 |
solute carrier family 25 member... |
84277 |
84277 |
DNAJC30 |
DnaJ heat shock protein family ... |
84300 |
84300 |
UQCC2 |
ubiquinol-cytochrome c reductas... |
847 |
847 |
CAT |
catalase [Source:HGNC Symbol;Ac... |
84701 |
84701 |
COX4I2 |
cytochrome c oxidase subunit 4I... |
863 |
863 |
CBFA2T3 |
CBFA2/RUNX1 partner transcripti... |
8801 |
8801 |
SUCLG2 |
succinate-CoA ligase GDP-formin... |
8802 |
8802 |
SUCLG1 |
succinate-CoA ligase GDP/ADP-fo... |
8803 |
8803 |
SUCLA2 |
succinate-CoA ligase ADP-formin... |
89 |
89 |
ACTN3 |
actinin alpha 3 [Source:HGNC Sy... |
891 |
891 |
CCNB1 |
cyclin B1 [Source:HGNC Symbol;A... |
9016 |
9016 |
SLC25A14 |
solute carrier family 25 member... |
9167 |
9167 |
COX7A2L |
cytochrome c oxidase subunit 7A... |
92014 |
92014 |
SLC25A51 |
solute carrier family 25 member... |
92259 |
92259 |
MRPS36 |
mitochondrial ribosomal protein... |
9377 |
9377 |
COX5A |
cytochrome c oxidase subunit 5A... |
9551 |
9551 |
ATP5MF |
ATP synthase membrane subunit f... |
9555 |
9555 |
MACROH2A1 |
macroH2A.1 histone [Source:HGNC... |
9650 |
9650 |
MTFR1 |
mitochondrial fission regulator... |
983 |
983 |
CDK1 |
cyclin dependent kinase 1 [Sour... |
9927 |
9927 |
MFN2 |
mitofusin 2 [Source:HGNC Symbol... |